| Titre | Contributiuon of spectral-domain optical coherence tomography in a case of familial occult macular dystrophy. |
| But | To document the interest of using spectral-domain optical coherence tomography (SD-OCT) for the diagnosis and for the comprehension of macular dysfunction in occult macular dystrophy (OMD). |
| Méthodes | OMD is characterized by a progressive decline of visual acuity with normal fundus, normal fundus auto-fluorescence and normal fluo-angiography. In this clinical context, abnormal mf-ERG remains until now the gold standard to allow the diagnosis of OMD. However, SD-OCT may demonstrate significant anatomic changes in the photoreceptors layer. Morphologic photoreceptors layer abnormalities were investigated with SD-OCT in a member of a family with OMD. |
| Résultats | The SD-OCT demonstrated a foveal well-defined disruption of the inner segment-outer segment junction of photoreceptors. |
| Conclusion | OMD is a rare macular disorder which is very difficult to diagnose. The diagnosis can be promoted by using SD-OCT, demonstrating a disruption of the photoreceptors layer. These OCT findings most probably participate in the pathophysiology of vision lowering associated with OMD. |
| Nom | PIENS |
| Initiales | I |
| Institut | hopital erasme |
| Ville | bruxelles |
| Nom | CORDONNIER |
| Initiales | M |
| Institut | hopital erasme |
| Ville | bruxelles |
| Nom | RASQUIN |
| Initiales | F |
| Institut | hopital erasme |
| Ville | bruxelles |