| Title | Atypical dural carotid cavernous sinus fistula presenting as direct carotid cavernous sinus fistula |
| Purpose | To report a case of spontaneous dural carotid cavernous sinus fistula (CCSF) with symptoms and signs similar to traumatic direct CCSF fistula. |
| Methods | Case report |
| Results | CCSF are abnormal communications between the carotid arterial system and the venous cavernous sinus. Most often they are classified as either direct o indirect (also named dural). Clinical manifestations of CCSF frequently involve ophthalmic abnormalities. Direct CCSF results from a direct connection between the intracavernous carotid artery and the cavernous sinus, while dural CCSF arises from abnormal shunts to the cavernous sinus from the meningeal branches of the carotid artery. Typically, signs and symptoms of direct fistulas have an acute onset and dramatic ophthalmologic consequences, while dural fistulas have a gradual onset and milder ophthalmologic consequences. Our patient had acute and severe symptoms. Unexpectedly, the arteriography diagnosed a dural CCSF. It also revealed a recent homolateral petrous sinus thrombosis that possibly prevented further posterior drainage of the fistula, precipitating anteriorly redirected high flow and favouring an acute and dramatic clinical onset. |
| Conclusion | Dural CCSF may have an acute onset and present signs and symptoms as severe as in direct CCSF if a local thrombotic event abruptly modifies its blood drainage. |
| Last name | ATTHA |
| Initials | E |
| Department | CUB hôpital Erasme |
| City | Brussels |
| Last name | Lubicz |
| Initials | B |
| Department | CUB hôpital Erasme |
| City | Brussels |
| Last name | Janssens |
| Initials | S |
| Department | CHU hôpital St Pierre |
| City | Brussels |
| Last name | Cordonnier |
| Initials | M |
| Department | CUB hôpital Erasme |
| City | Brussels |