Titel | Recurring hyphaema as the presenting symptom of a juvenile xanthogranuloma. |
Doel | To report a 13-month old infant with the typical juvenile xanthogranuloma (JXG) skin lesions. She presented to her ophthalmologist with recurrent hyphaema. A lesion of the iris was discovered in the inferior part. The natural history, histological features and treatment of the condition are discussed. |
Methodes | Case report and review of the medical literature. |
Resultaten | The diagnosis of JXG was made by biopsy of a skin lesion. Despite topical steroid drops and three subconjunctival steroid injections, there was no regression of the iris mass. The iris mass subsided after systemic corticosteroid therapy. |
Conclusie | Juvenile xanthogranuloma is a benign histiocytic cutaneous disorder mainly occurring in children but also affecting the eye. The iris is most commonly involved, but also eyelid, epibulbar lesions, corneal involvement and orbital involvement have been described. JXG of the optic nerve, disc, retina and choroid has rarely been reported. |
Naam | VANDEWALLE |
Initialen | E |
Instituut | University Hospitals Leuven |
Stad | Leuven |
Naam | Van Der Hauwaert |
Initialen | N |
Instituut | Sint Augustinus Hospital |
Stad | Antwerpen |
Naam | Casteels |
Initialen | I |
Instituut | University Hospitals Leuven |
Stad | Leuven |